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Naslov:Primary cutaneous CD4-positive small or medium T-cell lymphoproliferative disorder : a case report and literature review
Avtorji:ID Trčko, Katarina (Avtor)
ID Lukinovič, Nuša (Avtor)
ID Šekoranja, Daja (Avtor)
Datoteke:.pdf PDF - Predstavitvena datoteka, prenos (16,92 MB)
MD5: FFA6837544A02CB88CBBAA547906EB00
 
URL URL - Izvorni URL, za dostop obiščite https://acta-apa.mf.uni-lj.si/journals/acta-dermatovenerol-apa/papers/10.15570/actaapa.2024.29/actaapa.2024.29.pdf
 
Jezik:Angleški jezik
Tipologija:1.03 - Drugi znanstveni članki
Organizacija:Logo ZSD - Združenje slovenskih dermatovenerologov
Logo UKC LJ - Univerzitetni klinični center Ljubljana
Povzetek:Primary cutaneous CD4-positive small or medium T-cell lymphoproliferative disorder (PCSM-LPD) is characterized by a slow-growing and asymptomatic solitary plaque or tumor, usually involving the head, neck, or upper extremities. The diagnosis is established based on clinical presentation, histopathological features including pleomorphic morphology and CD4-positive immunophenotype of neoplastic T lymphocytes, and molecular analysis showing clonally rearranged T-cell receptor (TCR) genes. Plaques typical of mycosis fungoides are essentially absent. Treatment options include surgical excision, radiotherapy, and topical or intralesional steroids. Because the disease is indolent, aggressive diagnostic tests and systemic treatments are not recommended. We present a case of PCSM-LPD in a previously healthy young man that spontaneously regressed after a biopsy.
Ključne besede:primary cutaneous CD4-positive small or medium T-cell lymphoproliferative disorder, primary cutaneous lymphoma, T-cell lymphoma, lymphoproliferative disorder, spontaneous regression
Status publikacije:Objavljeno
Verzija publikacije:Objavljena publikacija
Poslano v recenzijo:16.09.2024
Datum sprejetja članka:11.10.2024
Datum objave:01.06.2025
Kraj izida:Ljubljana
Založnik:Združenje slovenskih dermatovenerologov
Leto izida:2025
Leto izvedbe:2025
Št. strani:str. 79-82
Številčenje:Vol. 34, issue 2
PID:20.500.12556/DiRROS-29885 Novo okno
UDK:616.5
ISSN pri članku:1318-4458
DOI:10.15570/actaapa.2024.29 Novo okno
COBISS.SI-ID:220499203 Novo okno
Avtorske pravice:Na spletni strani revije navedeno: Acta Dermatovenerologica Alpina, Pannonica et Adriatica (ISSN 1318-4458) is an open access medical journal published quarterly by the Association of Slovenian Dermatovenerologists (https://acta-apa.mf.uni-lj.si/index.php); Authors publishing in our journal retain copyright of their work under the Creative Commons Attribution License (CC BY 4.0). This license allows unrestricted use, distribution, and reproduction of the work in any medium, provided the original author(s) and copyright holder(s) are appropriately credited, and the original publication in the journal is properly cited, following established academic practices (https://acta-apa.mf.uni-lj.si/submissions.php).
Datum objave v DiRROS:09.06.2026
Število ogledov:229
Število prenosov:221
Metapodatki:XML DC-XML DC-RDF
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Gradivo je del revije

Naslov:Acta dermatovenerologica Alpina, Panonica et Adriatica
Skrajšan naslov:Acta dermatovenerolog. Alp. Panon. Adriat.
Založnik:Slovene Welding Society
ISSN:1318-4458
COBISS.SI-ID:31649024 Novo okno

Licence

Licenca:CC BY 4.0, Creative Commons Priznanje avtorstva 4.0 Mednarodna
Povezava:http://creativecommons.org/licenses/by/4.0/deed.sl
Opis:To je standardna licenca Creative Commons, ki daje uporabnikom največ možnosti za nadaljnjo uporabo dela, pri čemer morajo navesti avtorja.

Sekundarni jezik

Jezik:Ni določen
Ključne besede:primarna kožna CD4-pozitivna limfoproliferativna motnja iz malih ali srednje velikih celic T, primarni kožni limfom, T-celični limfom, limfoproliferativna motnja, spontana regresija


Zbirka

To gradivo je del naslednjih zbirk del:
  1. Acta dermatovenerologica Alpina, Panonica et Adriatica

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