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Title:Case report : congenital extrahepatic portocaval shunt presenting as pulmonary arterial hypertension in a pregnant patient
Authors:Harlander, Matevž (Author)
Badovinac, Maja (Author)
Markoska, Frosina (Author)
Salobir, Barbara (Author)
Štupnik, Tomaž (Author)
Dolenšek, Marija (Author)
Kern, Izidor (Author)
Gorjup, Vojka (Author)
Galiè, Nazzareno (Author)
Tipology:1.03 - Short Scientific Article
Organisation:Logo UKPBAG - University Clinic of Respiratory and Allergic Diseases Golnik
Abstract:Congenital extrahepatic portocaval shunt (CEPS) is a rare condition in which a rare congenital vascular anomaly of the portal system is present. CEPS may manifest as pulmonary arterial hypertension (PAH). When diagnosed and treated early, PAH can be reversible. We report a case of a previously asymptomatic woman, who manifested with severe pulmonary hypertension during pregnancy and was consequently diagnosed with CEPS. After unsuccessful medical treatment, urgent lung transplantation was done.
Keywords:pulmonary hypertension, pregnancy, congenital extrahepatic portocaval shunt, Abernethy malformation, pulmonary arterial hypertension
Year of publishing:2022
COBISS_ID:92131331 Link is opened in a new window
ISSN on article:2045-8940
DOI:10.1002/pul2.12008 Link is opened in a new window
Note:Nasl. z nasl. zaslona; Soavtorji: Maja Badovinac, Frosina Markoska, Barbara Salobir, Tomaž Štupnik, Marija Iča Dolenšek, Izidor Kern, Vojka Gorjup, Nazzareno Galiè; Opis vira z dne 5. 1. 2022; Št. članka: e12008;
Files:.pdf PDF - Presentation file, download (883,93 KB)
URL URL - Source URL, visit
Journal:Pulm. circ.
University of Chicago Press
Rights:© 2021 The Authors
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License:CC BY-NC 4.0, Creative Commons Attribution Non-Commercial 4.0 International
Description:A creative commons license that bans commercial use, but the users don’t have to license their derivative works on the same terms.
Licensing start date:03.01.2022