| Title: | Case report : congenital extrahepatic portocaval shunt presenting as pulmonary arterial hypertension in a pregnant patient |
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| Authors: | Harlander, Matevž (Author)
Badovinac, Maja (Author)
Markoska, Frosina (Author)
Salobir, Barbara (Author)
Štupnik, Tomaž (Author)
Dolenšek, Marija (Author)
Kern, Izidor (Author)
Gorjup, Vojka (Author)
Galiè, Nazzareno (Author) |
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| Language: | English |
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| Tipology: | 1.03 - Short Scientific Article |
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| Organisation: |  UKPBAG - University Clinic of Respiratory and Allergic Diseases Golnik |
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| Abstract: | Congenital extrahepatic portocaval shunt (CEPS) is a rare condition in which a rare congenital vascular anomaly of the portal system is present. CEPS may manifest as pulmonary arterial hypertension (PAH). When diagnosed and treated early, PAH can be reversible. We report a case of a previously asymptomatic woman, who manifested with severe pulmonary hypertension during pregnancy and was consequently diagnosed with CEPS. After unsuccessful medical treatment, urgent lung transplantation was done. |
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| Keywords: | pulmonary hypertension, pregnancy, congenital extrahepatic portocaval shunt, Abernethy malformation, pulmonary arterial hypertension |
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| Year of publishing: | 2022 |
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| Publisher: | Wiley |
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| Source: | ZDA |
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| COBISS_ID: | 92131331  |
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| UDC: | 616.1 |
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| ISSN on article: | 2045-8940 |
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| DOI: | 10.1002/pul2.12008 |
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| Note: | Nasl. z nasl. zaslona;
Soavtorji: Maja Badovinac, Frosina Markoska, Barbara Salobir, Tomaž Štupnik, Marija Iča Dolenšek, Izidor Kern, Vojka Gorjup, Nazzareno Galiè;
Opis vira z dne 5. 1. 2022;
Št. članka: e12008;
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| Views: | 231 |
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| Downloads: | 129 |
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| Files: |  PDF - Presentation file, download (883,93 KB)
 URL - Source URL, visit https://onlinelibrary.wiley.com/doi/epdf/10.1002/pul2.12008
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| | | Journal: | Pulm. circ.
University of Chicago Press
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| | | Metadata: |     |
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| Rights: | © 2021 The Authors |
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