Title: | Case report : congenital extrahepatic portocaval shunt presenting as pulmonary arterial hypertension in a pregnant patient |
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Authors: | ID Harlander, Matevž (Author) ID Badovinac, Maja (Author) ID Markoska, Frosina (Author) ID Salobir, Barbara (Author) ID Štupnik, Tomaž (Author) ID Dolenšek, Marija (Author) ID Kern, Izidor, Klinika Golnik (Author) ID Gorjup, Vojka (Author) ID Galiè, Nazzareno (Author) |
Files: | PDF - Presentation file, download (883,93 KB) MD5: 8F79C380723DA4C0061CA5D78AE67083
URL - Source URL, visit https://onlinelibrary.wiley.com/doi/epdf/10.1002/pul2.12008
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Language: | English |
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Typology: | 1.03 - Other scientific articles |
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Organization: | UKPBAG - University Clinic of Respiratory and Allergic Diseases Golnik
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Abstract: | Congenital extrahepatic portocaval shunt (CEPS) is a rare condition in which a rare congenital vascular anomaly of the portal system is present. CEPS may manifest as pulmonary arterial hypertension (PAH). When diagnosed and treated early, PAH can be reversible. We report a case of a previously asymptomatic woman, who manifested with severe pulmonary hypertension during pregnancy and was consequently diagnosed with CEPS. After unsuccessful medical treatment, urgent lung transplantation was done. |
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Keywords: | pulmonary hypertension, pregnancy, congenital extrahepatic portocaval shunt, Abernethy malformation, pulmonary arterial hypertension |
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Publication status: | Published |
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Publication version: | Version of Record |
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Place of publishing: | ZDA |
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Publisher: | Wiley |
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Year of publishing: | 2022 |
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Number of pages: | str. 1-4 |
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Numbering: | Vol. 12, iss. 1 |
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PID: | 20.500.12556/DiRROS-14709 |
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UDC: | 616.1 |
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ISSN on article: | 2045-8940 |
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DOI: | 10.1002/pul2.12008 |
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COBISS.SI-ID: | 92131331 |
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Copyright: | © 2021 The Authors |
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Note: | Nasl. z nasl. zaslona;
Soavtorji: Maja Badovinac, Frosina Markoska, Barbara Salobir, Tomaž Štupnik, Marija Iča Dolenšek, Izidor Kern, Vojka Gorjup, Nazzareno Galiè;
Opis vira z dne 5. 1. 2022;
Št. članka: e12008;
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Publication date in DiRROS: | 10.01.2022 |
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Views: | 1175 |
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Downloads: | 742 |
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