20.500.12556/DiRROS-14709 Case report : congenital extrahepatic portocaval shunt presenting as pulmonary arterial hypertension in a pregnant patient Congenital extrahepatic portocaval shunt (CEPS) is a rare condition in which a rare congenital vascular anomaly of the portal system is present. CEPS may manifest as pulmonary arterial hypertension (PAH). When diagnosed and treated early, PAH can be reversible. We report a case of a previously asymptomatic woman, who manifested with severe pulmonary hypertension during pregnancy and was consequently diagnosed with CEPS. After unsuccessful medical treatment, urgent lung transplantation was done. pulmonary hypertension pregnancy congenital extrahepatic portocaval shunt Abernethy malformation pulmonary arterial hypertension pljučna hipertenzija nosečnost prirojeni ekstrahepatični portokavalni šant Abernethyjev sindrom pljučna arterijska hipertenzija true false true Wiley Angleški jezik Ni določen © 2021 The Authors Neznano 2022-01-10 13:26:06 2022-01-10 13:26:07 2022-08-20 03:37:20 0000-00-00 00:00:00 2022 0 ZDA 0 Nasl. z nasl. zaslona; Soavtorji: Maja Badovinac, Frosina Markoska, Barbara Salobir, Tomaž Štupnik, Marija Iča Dolenšek, Izidor Kern, Vojka Gorjup, Nazzareno Galiè; Opis vira z dne 5. 1. 2022; Št. članka: e12008; str. 1-4 iss. 1 Vol. 12 Jan. 2021 0000-00-00 Zaloznikova Objavljeno NiDoloceno 0000-00-00 0000-00-00 0000-00-00 616.1 2045-8940 10.1002/pul2.12008 92131331 RAZ_Harlander_Matevz_i2022.pdf RAZ_Harlander_Matevz_i2022.pdf 1 8F79C380723DA4C0061CA5D78AE67083 17715d32d5370c645a9c11d879a1fd23b32f4b30ec69826d1b9b509fdc4cd0b8 cf084566-17b6-11ed-b6b8-001a4af901a5 https://dirros.openscience.si/Dokument.php?lang=slv&id=18897 https://onlinelibrary.wiley.com/doi/epdf/10.1002/pul2.12008 1 https://dirros.openscience.si/Dokument.php?lang=slv&id=18896 Univerzitetna klinika za pljučne bolezni in alergijo Golnik 0 0 0