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Naslov:Appendiceal neuroendocrine tumors in children and adolescents : the European Cooperative Study Group for Pediatric Rare Tumors (EXPeRT) diagnostic and therapeutic recommendations
Avtorji:ID Virgone, Calogero (Avtor)
ID Roganović, Jelena (Avtor)
ID Rindi, Guido (Avtor)
ID Kuhlen, Michaela (Avtor)
ID Jamšek, Jan (Avtor)
ID Panagopoulou, Paraskevi (Avtor)
ID Bajčiová, Viera (Avtor)
ID Ben-Ami, Tal (Avtor)
ID Raphael, Martine F. (Avtor)
ID Seitz, Guido (Avtor), et al.
Datoteke:.pdf PDF - Predstavitvena datoteka, prenos (682,66 KB)
MD5: 16C01D8D9698A2C48CBBFC9FADB1E842
 
URL URL - Izvorni URL, za dostop obiščite https://www.surgjournal.com/article/S0039-6060(25)00303-4/fulltext
 
Jezik:Angleški jezik
Tipologija:1.02 - Pregledni znanstveni članek
Organizacija:Logo UKC LJ - Univerzitetni klinični center Ljubljana
Povzetek:Neuroendocrine tumors of the appendix, formerly known as carcinoid tumors, represent a rare entity. They are slow-growing tumors, characterized by an indolent clinical course. In pediatric patients, the 5-year overall survival is estimated to be 100% and the event-free survival slightly less than 100%, with only one reported case of local relapse to date. Nevertheless, a proportion of these patients still undergo a second surgery, mostly represented by right hemicolectomy with mesenteric lymphadenectomy, in consideration of the presence of certain risk factors (size >1.5 or 2 cm; tumors of the appendiceal base with or without suspicious residuals, mesoappendiceal invasion, lymphovascular invasion, serosal breach). This approach represents an overtreatment of patients with a benign clinical course regardless of the presence of risk factors and/or whether a second surgery is performed. National recommendations for diagnosis, treatment, and follow-up of neuroendocrine tumors of the appendix in pediatric age are available in France, Italy, and Germany, but international consensus is lacking. This review presents the internationally harmonized recommendations for the diagnosis and treatment of neuroendocrine tumors of the appendix in children and adolescents, established by the European Cooperative Study Group for Pediatric Rare Tumors group.
Ključne besede:appendiceal neuroendocrine tumors, pediatric oncology, diagnostic and therapeutic recommendations
Status publikacije:Objavljeno
Verzija publikacije:Objavljena publikacija
Leto izida:2025
Št. strani:8 str.
Številčenje:Vol. 184, [article no.] 109451
PID:20.500.12556/DiRROS-28839 Novo okno
UDK:616-053.2:616-006
ISSN pri članku:1532-7361
DOI:10.1016/j.surg.2025.109451 Novo okno
COBISS.SI-ID:274631427 Novo okno
Opomba:Nasl. z nasl. zaslona; Opis vira z dne 9. 4. 2026;
Datum objave v DiRROS:09.04.2026
Število ogledov:126
Število prenosov:89
Metapodatki:XML DC-XML DC-RDF
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Gradivo je del revije

Naslov:Surgery
Skrajšan naslov:Surgery
Založnik:Mosby
ISSN:1532-7361
COBISS.SI-ID:3618068 Novo okno

Licence

Licenca:CC BY-NC-ND 4.0, Creative Commons Priznanje avtorstva-Nekomercialno-Brez predelav 4.0 Mednarodna
Povezava:http://creativecommons.org/licenses/by-nc-nd/4.0/deed.sl
Opis:Najbolj omejujoča licenca Creative Commons. Uporabniki lahko prenesejo in delijo delo v nekomercialne namene in ga ne smejo uporabiti za nobene druge namene.

Sekundarni jezik

Jezik:Slovenski jezik
Ključne besede:apendikularni nevroendokrini tumorji, pediatrična onkologija, diagnostična in terapevtska priporočila


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