20.500.12556/DiRROS-31289 Obravnava otrok in mladostnikov s hipertrofično kardiomiopatijo - pregled literature in izkušnje slovenskega centra Management of children and adolescents with hypertrophic cardiomyopathy - literature review and experiences of a Slovenian center Hipertrofična kardiomiopatija je druga najpogostejša oblika kardiomiopatije pri otrocih. V pediatrični populaciji gre za izrazito heterogeno skupino bolezni, ki ima pogosto genetske vzroke ali sodi v sklop osnovne sindromske oz. kronične sistemske bolezni. Namen prispevka je opisati etiologijo in klinično sliko bolezni ter pristop k diagnosticiranju in zdravljenju hipertrofične kardiomiopatije z opisom izkušenj pri obravnavi otrok s hipertrofično kardiomiopatijo na oddelku Službe za kardiologijo Pediatrične klinike Ljubljana. Hypertrophic cardiomyopathy is the second most common form of cardiomyopathy in children. It represents a highly heterogeneous group of disorders that is often genetically determined or associated with an underlying syndromic or chronic systemic condition. This article aims to describe the etiology and clinical presentation of the disease, as well as the diagnostic and therapeutic approach to hypertrophic cardiomyopathy, supplemented by our own experience in the management of children with this condition. sarkomerna kardiomiopatija srčno popuščanje nenadna srčna smrt MRI srca fibroza sarcomeric cardiomyopathy heart failure sudden cardiac death cardiac MRI fibrosis true false true Slovenski jezik Angleški jezik Neznano 2026-07-24 09:33:38 2026-07-24 09:33:38 2026-07-25 03:45:58 0000-00-00 00:00:00 2026 0 0 Nasl. z nasl. zaslona; Opis vira z dne 24. 7. 2026; Besedilo v slov.; str. 134-145 no. 5/6 Vol. 95 2026 0000-00-00 Zaloznikova Objavljeno NiDoloceno 0000-00-00 0000-00-00 0000-00-00 616.1 1581-0224 10.6016/ZdravVestn.3684 285928195 RAZ_Sluga_Metka_2026.pdf RAZ_Sluga_Metka_2026.pdf 1 AA0290562443558319D4F44647F95820 3d2f486e19ab621dd7351fd7234fe7882c17a7ef0858f287811c3dda8501247b 169c47b2-8732-11f1-812a-001a4af901a5 https://dirros.openscience.si/Dokument.php?lang=slv&id=48355 https://vestnik.szd.si/index.php/ZdravVest/article/view/3684 1 fef3463c-8731-11f1-812a-001a4af901a5 https://dirros.openscience.si/Dokument.php?lang=slv&id=48354 Univerzitetni klinični center Ljubljana 0 0 0